04580nam a2200325Mc 4500001001300000005001700013008004100030010001700071020002700088020001500115035002200130040004400152041000800196060001100204100002900215245052900244250002200773260005000795300003900845505156000884520156302444546002204007650004904029650003104078650004804109650001504157650002204172700003204194765002804226on100427395520180313061229.0171020s2016 nyu 000 0 eng d a 2015008911 a9780071752503 (2a.Ed.) z0071752501 a(OCoLC)1004273955 aCo-BoUCMbgercSaul NiñodSaul Niño0 aeng 0aWE 5501 aAmato, Anthony A.d1960-10aNeuromuscular disorderscAnthony A. Amato, MD, Vice-Chairman, Department of Neurology, Chief, Neuromuscular Divbision, Brigham and Women's Hospital, Boston, Massachusetts, Harvard Medical School, Boston, Massachusetts, James A. Russell, DO, FAAN, Vice Chairman, Department of Neurology, Lahey Hospital & Medical Center, Director, ALS Clinic, Lahey Hospital & Medical Center, Chairman, Ethics Center, Lahey Hospital & Medical Center, Clinical Professor of Neurology, Tufts University School of Medicine, Boston, Massachusetts aSegunda edición3 aNew YorkbMcGraw-Hill Education Medicalc2016 aviii, 948 páginasbilustraciones0 aApproach to patients with neuromuscular diseaseTesting in neuromuscular disease -- Muscle and nerve histopathology -- Principles of immunomodulating treatment -- The rehabilitation of neuromuscular diseases / Sabrina Paganoni and Erik Ensrud -- Amyotrophic lateral sclerosis -- Hereditary spastic paraparesis -- Spinal muscular atrophies -- Other motor neuron disorders -- Disorders of motor nerve hyperactivity -- Charcot-Marie-Tooth disease and related disorders -- Other hereditary neuropathies -- Guillain-Barré syndrome and related disorders -- Chronic inflammatory demyelinating polyradiculoneuropathy and related neuropathies -- Vasculitic neuropathies -- Neuropathies associated with systemic disease -- Neuropathies associated with infections -- Neuropathies related to nutritional deficiencies -- Neuropathies associated with malignancy -- Toxic neuropathies -- Neuropathies associated with endocrinopathies -- Idiopathic polyneuropathy -- Cervical and thoracic radiculopathies, brachial plexopathies, and mononeuropathies of the arm -- Focal neuropathies of the lower extremities : radiculopathies, plexopathies, and mononeuropathies -- Autoimmune myasthenia gravis -- Other disorders of neuromuscular transmission -- Muscular dystrophies -- Congenital myopathies -- Metabolic myopathies -- Mitochondrial disorders -- Myotonic dystrophies -- Nondystrophic myotonias and periodic paralysis -- Inflammatory myopathies -- Myopathies associated with systemic disease -- Toxic myopathies -- Neuromuscular mimics / Sabrina Paganoni and Erik Ensrud. aApproach to patients with neuromuscular disease -- Testing in neuromuscular disease -- Muscle and nerve histopathology -- Principles of immunomodulating treatment -- The rehabilitation of neuromuscular diseases / Sabrina Paganoni and Erik Ensrud -- Amyotrophic lateral sclerosis -- Hereditary spastic paraparesis -- Spinal muscular atrophies -- Other motor neuron disorders -- Disorders of motor nerve hyperactivity -- Charcot-Marie-Tooth disease and related disorders -- Other hereditary neuropathies -- Guillain-Barré syndrome and related disorders -- Chronic inflammatory demyelinating polyradiculoneuropathy and related neuropathies -- Vasculitic neuropathies -- Neuropathies associated with systemic disease -- Neuropathies associated with infections -- Neuropathies related to nutritional deficiencies -- Neuropathies associated with malignancy -- Toxic neuropathies -- Neuropathies associated with endocrinopathies -- Idiopathic polyneuropathy -- Cervical and thoracic radiculopathies, brachial plexopathies, and mononeuropathies of the arm -- Focal neuropathies of the lower extremities : radiculopathies, plexopathies, and mononeuropathies -- Autoimmune myasthenia gravis -- Other disorders of neuromuscular transmission -- Muscular dystrophies -- Congenital myopathies -- Metabolic myopathies -- Mitochondrial disorders -- Myotonic dystrophies -- Nondystrophic myotonias and periodic paralysis -- Inflammatory myopathies -- Myopathies associated with systemic disease -- Toxic myopathies -- Neuromuscular mimics / Sabrina Paganoni and Erik Ensrud aTexto en inglés17aEnfermedades neuromusculares xDiagnostíco27aDiagnóstico diferencial 27aTécnicas y procedimientos diagnósticos  7aOrtopedia  7aRehabilitación 1 aRussell, James Adamsd1951- tNeuromuscular disorders